Intravenous Anesthesia in a Rare Pediatric Patient with Poland Syndrome: Case Report
##semicolon##
https://doi.org/10.59188/eduvest.v6i3.52349##semicolon##
pediatric anesthesia##common.commaListSeparator## Poland syndrome##common.commaListSeparator## intravenous anesthesia##common.commaListSeparator## malignant hyperthermia##common.commaListSeparator## general anesthesiaAbstrakt
Poland syndrome (PS) is a very rare congenital anomaly characterized by hypoplasia or aplasia of the pectoral muscles and mammary hypoplasia and is associated with anomalies in the ipsilateral region of the body. Poland syndrome can increase the risk of developing intraoperative malignant hyperthermia; hence, special consideration is needed in the management of anesthesia in these patients. We report herein the management of general anesthesia for syndactyly release surgery in a child with Poland syndrome. A 1-year- and 11-month-old boy with Poland syndrome was scheduled to undergo manus dextra interphalangeal syndactyly release surgery under total intravenous general anesthesia using midazolam (0.1 mg/kg body weight), fentanyl (2 mcg/kg), and atracurium (0.5 mg/kg body weight) as induction agents, with maintenance using midazolam (0.3 mg/kg/h). Anesthesia can be performed at this age to prevent contractures and deformities and to avoid functional abnormalities. The anesthesia lasted 120 min with intraoperatively stable hemodynamics. After the operation, the patient was treated in a regular ward and discharged after 2 days of treatment. The use of total intravenous anesthesia with midazolam in children with Poland syndrome for the surgical release of manus dextra interphalangeal syndactyly is a good option and is also clinically beneficial.
##submission.citations##
Anderson, B. J., & Bagshaw, O. (2019). Practicalities of total intravenous anesthesia and target-controlled infusion in children. Anesthesiology, 131(1), 164–185. https://doi.org/10.1097/ALN.0000000000002657
Baldelli, I., Baccarani, A., Barone, C., Bedeschi, F., Bianca, S., Calabrese, O., Castori, M., Catena, N., Corain, M., Costanzo, S., Barbato, G. D. P., De Stefano, S., Divizia, M. T., Feletti, F., Formica, M., Lando, M., Lerone, M., Lorenzetti, F., Martinoli, C., ... Crimi, M. (2020). Consensus based recommendations for diagnosis and medical management of Poland syndrome (sequence). Orphanet Journal of Rare Diseases, 15(1), 1–17. https://doi.org/10.1186/s13023-020-01481-x
Buonsenso, D., Piazza, M., Boner, A. L., & Bellanti, J. A. (2022). Long COVID: A proposed hypothesis-driven model of viral persistence for the pathophysiology of the syndrome. Allergy and Asthma Proceedings, 43(3), 187.
Course, F. C. A. R., & Mogane, P. (2022). Paediatric total intravenous anaesthesia and target-controlled infusion. Southern African Journal of Anaesthesia and Analgesia, 28(5), 55–60.
Cowie, P., Baxter, A., & McCormack, J. (2019). Total intravenous anaesthesia in children: A practical guide. Anaesthesia and Intensive Care Medicine, 20(6), 348–352. https://doi.org/10.1016/j.mpaic.2019.03.002
Cui, L., Li, S., Wang, S., Wu, X., Liu, Y., Yu, W., Wang, Y., Tang, Y., Xia, M., & Li, B. (2024). Major depressive disorder: hypothesis, mechanism, prevention and treatment. Signal Transduction and Targeted Therapy, 9(1), 30.
Díaz-Crespo, J., Vázquez-Mambrilla, Y., & García-Herrera, F. (2017). Anestesia general en paciente con síndrome de Poland. Revista Española de Anestesiología y Reanimación, 64(2), 112–115. https://doi.org/10.1016/j.redar.2016.07.008
Ellinas, H., & Albrecht, M. A. (2020). Malignant hyperthermia update. Anesthesiology Clinics, 38(1), 165–181. https://doi.org/10.1016/j.anclin.2019.10.010
Fiterman Rodrigues, R., Castro de Lima, R., Araujo Rayol, G., Silva Gomes de Oliveira, E. J., Rey Moura, E. C., Barros de Oliveira, C. M., de Sousa Gomes, L. M. R., & Cunha Leal, P. da. (2020). Total intravenous anesthesia in a patient with Poland syndrome submitted to video-laparoscopic inguinal hernioplasty: A case report. International Journal of Case Reports and Images, 11, 1. https://doi.org/10.5348/101163z01rr2020cr
Gui, L., Shen, S., & Mei, W. (2018). Anaesthesia for chest wall reconstruction in a patient with Poland syndrome: CARE-compliant case report and literature review. BMC Anesthesiology, 18(1), 1–8. https://doi.org/10.1186/s12871-018-0518-4
Gupta, A., & Kalra, B. (2021). Anaesthetic challenges and difficult airway in a child with Poland's syndrome. Indian Journal of Clinical Anaesthesia, 8(3), 479–482. https://doi.org/10.18231/j.ijca.2021.091
Hashim, E. A. A., Quek, B. H., & Chandran, S. (2021). A narrative review of Poland's syndrome: Theories of its genesis, evolution and its diagnosis and treatment. Translational Pediatrics, 10(4), 1008–1019. http://dx.doi.org/10.21037/tp-20-386
Hopkins, P. M. (2011). Malignant hyperthermia: Pharmacology of triggering. British Journal of Anaesthesia, 107(1), 48–56. https://doi.org/10.1093/bja/aer132
Jun, Y. E., Jung, Y. D., Kang, L. K., & Kim, K. N. (2023). Anesthetic management of a patient with Poland's syndrome: A case report. European Journal of Medical and Health Sciences, 5(4), 3–5. http://dx.doi.org/10.24018/ejmed.2023.5.4.1416
Kamran, M., Bibi, F., ur. Rehman, A., & Morris, D. W. (2022). Major depressive disorder: existing hypotheses about pathophysiological mechanisms and new genetic findings. Genes, 13(4), 646.
Lotfy, M. A., Ayaad, M. G., Elsawaf, M. I., & Atyia, G. F. (2021). Continuous midazolam infusion can minimize the pro-inflammatory response to anesthesia and surgery for pediatric patients with intra-abdominal infection: Comparative study versus continuous propofol infusion. Egyptian Journal of Anaesthesia, 37(1), 337–342. https://doi.org/10.1080/11101849.2021.1955532
Romanini, M. V., Calevo, M. G., Puliti, A., Vaccari, C., Valle, M., Senes, F., & Torre, M. (2018). Poland syndrome: A proposed classification system and perspectives on diagnosis and treatment. Seminars in Pediatric Surgery, 27(3), 189–199. https://doi.org/10.1053/j.sempedsurg.2018.05.007
Sabourdin, N., Louvet, N., & Constant, I. (2015). Selection of anesthesia techniques for the neonate. In Neonatal anesthesia (pp. 131–152). Springer. https://doi.org/10.1007/978-1-4419-6041-2
Sardescu, G., Dan, A., & Comandașu, D.-E. (2017). Poland syndrome - case report and literature review. Perinatologia, 1(1), 44. https://doi.org/10.26416/peri.1.1.2017.480
Yang, L., Tautz, T., Zhang, S., Fomina, A., & Liu, H. (2020). The current status of malignant hyperthermia. Journal of Biomedical Research, 34(2), 75–85. https://doi.org/10.7555/JBR.33.20180089
##submission.downloads##
Publikované
##submission.howToCite##
Číslo
Sekcia
##submission.license##
##submission.copyrightStatement##
##submission.license.cc.by-sa4.footer##
